Congenital cystic adenomatoid malformation associated with right aortic arch with mirror image branching and absence of left pulmonary artery in an adult

Abstract Background Congenital cystic adenomatoid malformation is an uncommon developmental anomaly that diagnosed prenatally or during early childhood and rare to present in adulthood. Type 2 congenital often associated with other anomalies such as cardiac anomalies. We a case of type adult male absence left pulmonary artery right aortic arch mirror image branching. To our knowledge, this the first report combination all three Case presentation A 33-year-old presented Department Pulmonary Medicine high-grade fever, chills rigor, breathlessness, productive cough for duration one week. He had multiple similar self-limiting episodes past which did not require hospitalization. The plain radiograph showed small hilum. CT thorax lesions size 0.5–2.0 cm apico-posterior segment upper lobe; anterior, posterior, lateral segments lower apical lobe maximal cyst wall thickness mm. Volume lung was reduced trans-thoracic herniation medial middle bronchiectatic changes were seen apical, posterior fibrotic strands lobe. Mediastinal window right-sided trunk continue absent artery. Conclusions Though disease infancy childhood, it should also be considered adults presenting recurrent respiratory tract infections and/or pneumothorax. Radiologists must aware types adenomatous (CCAM) their associations, CCAM has high association disease. Proximal interruption if continues either